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Athetoid Movements as Initial Manifestation of Primary Sjögren Syndrome

Alvarado-Franco, Norma L.; Gonzalez-Marques, Catalina; Olguin-Ramirez, Leticia A.; Garza-Alpirez, Alejandro; Femat-Roldan, Giovana; Martinez-Ramirez, Daniel

Background: Primary Sjögren syndrome (pSS) is an autoimmune disorder characterized by exocrine gland and extraglandular symptoms. We present a case report of pSS with an initial presentation of athetoid movements.

Case Report: A 74-year-old female presented with a 2-month history of slow undulating movements in her trunk and thighs that eventually spread to her neck and lower extremities. She also reported dry eyes, dry mouth, as well as pain in her shoulders and thighs. Her proinflammatory markers and rheumatologic profile were positive. Her salivary gland biopsy revealed a Focus score > 2. Brain magnetic resonance imaging was normal. A diagnosis of pSS was made. The patient’s symptoms improved with hydroxychloroquine, pilocarpine, gabapentin, and clonazepam.

Discussion: Clinicians should consider and screen for primary autoimmune disorders as a cause of subacute athetoid movements in elderly patients. Although aggressive treatment has been recommended, treatment should be tailored to each patient’s specific needs.

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Title
Tremor and Other Hyperkinetic Movements
DOI
https://doi.org/10.7916/D8HQ5GHB

More About This Work

Academic Units
Center for Parkinson's Disease and Other Movement Disorders
Published Here
February 14, 2019
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