A Case of Myoclonus–Dystonia Responding to Low-frequency Pallidal Stimulation

Sarva, Harini; Miravite, Joan; Swan, Matthew C.; Deik, Andres; Raymond, Deborah; Severt, William L.; Kopell, Brian H.

Background: High frequency pallidal stimulation has been shown to improve various types of dystonia, including myoclonus-dystonia.

Case Report: We report a case of epsilon sarcoglycan mutation-negative myoclonus-dystonia (MD) with response to low frequency bilateral pallidal stimulation.

Discussion: Low frequency pallidal stimulation provides an effective means of treating various dystonias, regardless of genetic status, as in our case, as it provides increased programming options with less adverse effects.


Also Published In

Tremor and Other Hyperkinetic Movements

More About This Work

Academic Units
Center for Parkinson's Disease and Other Movement Disorders
Published Here
November 22, 2017