1. Inhibitory-excitatory imbalance in hippocampal subfield cornu ammonis 2 circuitry in a mouse model of temporal lobe epilepsy Whitebirch, Alexander Craig 2021 Theses NeurosciencesTemporal lobe epilepsyMiceDentate gyrusHippocampus (Brain)ConvulsionsNervous system--DegenerationSynapses
2. Autophagy-linked FYVE protein mediates the turnover of mutant huntingtin and modifies pathogenesis in mouse models of Huntington’s disease Fox, Leora Mestel 2016 Theses Nervous system--DegenerationHuntington's diseaseProtein-protein interactionsNeurosciences
3. A Stem Cell Model of the Motor Circuit Reveals Distinct Requirements for SMN in Motor Neuron Survival and Function Janas, Anna 2015 Theses Neural circuitryNervous system--DegenerationSpinal muscular atrophyMotor neuronsNeurosciences
4. Characterization of motor pool selectivity of neuromuscular degeneration and identification of molecular correlates of disease resistance in Type I spinal muscular atrophy Lee, Justin 2015 Theses Spinal muscular atrophyNervous system--DegenerationNeuromuscular diseasesNeurosciencesPathologyBiology
5. Mechanisms of FUS-mediated motor neuron degeneration in amyotrophic lateral sclerosis Lyashchenko, Alex 2015 Theses Motor neuronsMotor neurons--DiseasesNervous system--DegenerationAmyotrophic lateral sclerosisNeurosciences
6. Role of Gigaxonin in the Regulation of Intermediate Filaments: a Study Using Giant Axonal Neuropathy Patient-Derived Induced Pluripotent Stem Cell-Motor Neurons Johnson-Kerner, Bethany 2013 Theses Cytoplasmic filamentsNervous system--DiseasesNervous system--DegenerationMotor neuronsNeuropathyNeurosciencesCytology
7. Modeling Alzheimer's Disease Using Cellular Reprogramming Technologies Chau, Lily 2012 Theses NeurosciencesAlzheimer's diseaseCytologyNervous system--Degeneration